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Patient Presentation: A 23-year-old obese female was diagnosed with idiopathic intracranial hypertension (IIH) and referred to neurosurgery for ventriculoperitoneal shunt. A baseline ocular examination was performed prior to the procedure.
On examination, vision was 20/200 in the right eye, and 20/40 in the left eye. There was a right relative afferent pupillary defect. Slit lamp examination was normal.
A dilated fundus examination was performed demonstrating the following:
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Retina
Case 41
Patient Presentation: A 6-year-old asymptomatic male was referred for bilateral macular lesions. Visual acuity was 20/30 –2 OD and 20/25 -2 OS. Fundus photo and OCT OU were performed and shown below.
Question: What is the main abnormality see on the patient's OCT images?
Question: What important question should you ask?
Question: What is the best next step?
Question: What is the most likely diagnosis?
Question: What stage of Best Vitelliform Macular Dystrophy is shown in this case?
Question: How should this patient be managed?
References:
1.Parodi MB, Iacono P, Romano F, Bandello F. Spectral domain optical coherence tomography features in different stages of best vitelliform macular dystrophy. Retina. 2018 May 1;38(5):1041-6.
Learning Objectives:
1. To recognize and diagnose BVMD on OCT and fundoscopy
2. To understand the management plan for patients with BVMD and their families
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